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    &beta;-Hydroxyisovaleric Acid-d8
    產(chǎn)品基本信息
    產(chǎn)品編號:H943607
    產(chǎn)品名稱:&beta;-Hydroxyisovaleric Acid-d8
    產(chǎn)品CAS:123743-99-7
    規(guī)格含量:100mg
    產(chǎn)品價格:面議
    聯(lián)系我們:
    產(chǎn)品詳細介紹
    標準品編號: H943607
    名稱: β-Hydroxyisovaleric Acid-d8
    別名: 3-Hydroxy-3-methylbutanoic Acid-d8; 3-Hydroxy-3-methylbutyric Acid-d8; 3-Hydroxyisovaleric Acid-d8; β-Hydroxy-β-methylbutyric Acid-d8
    CAS號: 123743-99-7
    參考CAS號: Unlabelled: 625-08-1
    分子式: C?H?D?O?
    外觀: Colourless to Yellow Oil
    熔點: N/A
    分子量: 126.18
    儲存: 冰箱
    溶解度: Chloroform (Slightly), DMSO (Sparingly), Methanol (Slightly)
    種類: Building Blocks; Isotopic Labeled Analogues; Pharmaceutical/API Drug Impurities/Metabolites;
    應(yīng)用: β-Hydroxyisovaleric Acid-d8 is the isotope labelled analog of β-Hydroxyisovaleric Acid (H943605); a metabolite of the essential amino acid Leucine. It is synthesized in the human body and studies suggest that β-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated β-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.
    危險品: Not a dangerous good if item is equal to or less than 1g/ml and there is less than 100g/ml in the package
    參考文獻


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